Poster Presentation GENEMAPPERS 2024

Uncovering the Causes of Monogenic Parkinson’s Disease Among Individuals from Underrepresented Backgrounds in Australia and Mexico (#97)

Victor Flores Ocampo 1 2 , Miguel Enrique Renteria Rodriguez 1 2 , Kishore Raj Kumar 3 4 5 , Claudia Gonzaga Jauregui 6 , Natalia Soledad Ogonowski 1 2
  1. Mental Health & Neuroscience Program, QIMR Berghofer Medical Research Institute, Brisbane, QLD, Australia
  2. School of Biomedical Sciences, Faculty of Medicine, The University of Queensland, Brisbane, QLD, Australia
  3. Molecular Medicine Laboratory and Department of Neurology, Concord Repatriation General Hospital, Concord, NSW, Australia
  4. Faculty of Medicine and Health, The University of Sydney, Sydney, NSW, Australia
  5. Garvan Institute of Medical Research, Sydney, NSW, Australia
  6. International Laboratory for Human Genome Research, Laboratorio Internacional de Investigación sobre el Genoma Humano, Universidad Nacional Autónoma de México, Queretaro, Mexico

Introduction: Parkinson's Disease (PD) is a progressive neurodegenerative disorder affecting 2-3% of the global population over 65 years [1]. Its prevalence is increasing worldwide in both developed and developing countries. Previous research has been predominantly focused on populations of European descent, limiting the applicability of findings to global populations [2,3]. PD exhibits a complex genetic etiology encompassing both idiopathic and familial forms, with familial cases believed to be monogenic and accounting for 5-10% of all instances [4]. The Australian Parkinson’s Genetics Study (APGS), Monogenic Parkinson’s Disease Australia (MonoPDAus), and the MEX-PD Project, under the Global Parkinson’s Genetics Program (GP2), aim to elucidate the genetic underpinnings of PD across diverse populations.

Objectives: This study utilises data from APGS/MonoPDAus and MEX-PD to (i) identify patients with suspected familial PD, based on early age of onset and/or family history; (ii) identify novel pathogenic variants and genes associated with monogenic PD, particularly among underrepresented groups; (iii) establish genotype-phenotype correlations for PD genes and their clinical manifestations; (iv) apply a consistent analysis workflow across Australian and Mexican cohorts.

Methods: We will prioritise 1,000 APGS participants with positive family history and/or early-onset PD for whole-genome sequencing, with a focus on diverse Australian population groups. Similarly, 68 participants from MEX-PD, identified as potential monogenic PD cases, will also undergo this process. For both groups, neurologists and movement disorder specialists will recontact and assess patients to gather phenotypic data and biological samples. The clinical and genetic data will undergo quality control, and analysis using bioinformatic pipelines to identify, annotate, prioritise, interpret, curate, and validate known and novel pathogenic variants, as well as candidate genes associated with monogenic PD.

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  2. Rodríguez-Violante M, Velásquez-Pérez L, Cervantes-Arriaga A. Incidence rates of Parkinson’s disease in Mexico: Analysis of 2014-2017 statistics. Rev Mex Neuroci. 2019;20: 136–140.
  3. Bivol S, Mellick GD, Gratten J, Parker R, Mulcahy A, Mosley PE, et al. Australian Parkinson’s Genetics Study (APGS): pilot (n=1532). BMJ Open. 2022;12: e052032.
  4. Lesage S, Brice A. Parkinson’s disease: from monogenic forms to genetic susceptibility factors. Hum Mol Genet. 2009;18: R48–59.